A rare case of retropharyngeal fibromatosis presenting with stridor

Stridor is one of the common emergencies in otolaryngology clinics, usual causes being malignancies glottis and hypopharynx. We present a rare case stridor caused by retropharyngeal fibromatosis an elderly patient. A 62-year-old male patient presented with complaints breathing difficulty associated dysphagia for one-month duration. On evaluation, he was found to have moderate smooth mucosa-covered bulge posterior pharyngeal wall obscuring endolarynx. With working diagnosis mass causing stridor, underwent emergency tracheostomy. Initial punch biopsies from lesion were non-diagnostic. further evaluation imaging histopathological examination incisional biopsy, we arrived at giant extending skull base C6. The en-bloc trans-cervical excision tumor. Fibromatoses retropharynx group tumor entity, which benign, locally aggressive recurrent. Dysphagia presentation though large tumors can due upper airway obstruction. Imaging preoperative surgical planning play crucial role individualizing management these their inaccessible location proximity major vasculature nerves head neck. Complete, meticulous pre-operative followed paramount importance treatment thereby prevent its recurrence.